Tags

Type your tag names separated by a space and hit enter

Anesthetic Considerations for an Adult Patient with Freeman-Sheldon Syndrome Undergoing Open Heart Surgery.
Case Rep Anesthesiol 2018; 2018:7862327CR

Abstract

Freeman-Sheldon syndrome (FSS) or "whistling face" syndrome is a rare congenital disorder complicated by characteristic facial deformities and muscular contractures. We report on a 64-year-old male patient presenting for surgical replacement of his aortic valve and review the available literature on anesthetic considerations and perioperative management principles. FSS frequently poses a significant challenge to airway management and gaining vascular access. Moreover, these patients are reportedly at risk for developing malignant hyperthermia (MH) or neuroleptic malignant syndrome.

Authors+Show Affiliations

Department of Anesthesiology and Critical Care Medicine, MediClin Heart Institute Lahr/Baden, Lahr, Germany.Department of Anesthesiology and Critical Care Medicine, MediClin Heart Institute Lahr/Baden, Lahr, Germany.Department of Cardiac Surgery, MediClin Heart Institute Lahr/Baden, Lahr, Germany.Department of Cardiac Surgery, MediClin Heart Institute Lahr/Baden, Lahr, Germany.Department of Cardiac Surgery, MediClin Heart Institute Lahr/Baden, Lahr, Germany.Department of Anesthesiology and Critical Care Medicine, MediClin Heart Institute Lahr/Baden, Lahr, Germany.

Pub Type(s)

Case Reports

Language

eng

PubMed ID

29666709

Citation

Viehmeyer, S, et al. "Anesthetic Considerations for an Adult Patient With Freeman-Sheldon Syndrome Undergoing Open Heart Surgery." Case Reports in Anesthesiology, vol. 2018, 2018, p. 7862327.
Viehmeyer S, Gabriel P, Bauer K, et al. Anesthetic Considerations for an Adult Patient with Freeman-Sheldon Syndrome Undergoing Open Heart Surgery. Case Rep Anesthesiol. 2018;2018:7862327.
Viehmeyer, S., Gabriel, P., Bauer, K., Bauer, S., Sodian, R., & Hilberath, J. N. (2018). Anesthetic Considerations for an Adult Patient with Freeman-Sheldon Syndrome Undergoing Open Heart Surgery. Case Reports in Anesthesiology, 2018, p. 7862327. doi:10.1155/2018/7862327.
Viehmeyer S, et al. Anesthetic Considerations for an Adult Patient With Freeman-Sheldon Syndrome Undergoing Open Heart Surgery. Case Rep Anesthesiol. 2018;2018:7862327. PubMed PMID: 29666709.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Anesthetic Considerations for an Adult Patient with Freeman-Sheldon Syndrome Undergoing Open Heart Surgery. AU - Viehmeyer,S, AU - Gabriel,P, AU - Bauer,K, AU - Bauer,S, AU - Sodian,R, AU - Hilberath,J N, Y1 - 2018/02/13/ PY - 2017/11/16/received PY - 2018/01/16/accepted PY - 2018/4/19/entrez PY - 2018/4/19/pubmed PY - 2018/4/19/medline SP - 7862327 EP - 7862327 JF - Case reports in anesthesiology JO - Case Rep Anesthesiol VL - 2018 N2 - Freeman-Sheldon syndrome (FSS) or "whistling face" syndrome is a rare congenital disorder complicated by characteristic facial deformities and muscular contractures. We report on a 64-year-old male patient presenting for surgical replacement of his aortic valve and review the available literature on anesthetic considerations and perioperative management principles. FSS frequently poses a significant challenge to airway management and gaining vascular access. Moreover, these patients are reportedly at risk for developing malignant hyperthermia (MH) or neuroleptic malignant syndrome. SN - 2090-6382 UR - https://www.unboundmedicine.com/medline/citation/29666709/Anesthetic_Considerations_for_an_Adult_Patient_with_Freeman-Sheldon_Syndrome_Undergoing_Open_Heart_Surgery L2 - https://dx.doi.org/10.1155/2018/7862327 DB - PRIME DP - Unbound Medicine ER -