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Poikilodermatous Mycosis Fungoides - Rare Entity, Different Treatment Modalities.
Acta Dermatovenerol Croat. 2018 Apr; 26(1):48-52.AD

Abstract

Poikilodermatous mycosis fungoides (PMF) is a rare clinical variant of early-stage MF with peculiar histological features. Poikiloderma occurs in many different clinical conditions, which makes a diagnostic procedure more complicated. PMF belongs to a group of MF variants with low risk of disease progression. We report a case of a 64-year-old woman, who presented with mottled skin aspect of erythema, poikilodermatous patches (hypopigmentation, hyperpigmentation, atrophy, and telangiectasia) on more than 80% of the body. Based on clinical, histopathological, and immunohistochemical findings, we established the diagnosis of PMF. Staging procedure determined stage IIA. As skin-directed therapy was the treatment of choice, the patient was successfully treated with psoralen-UVA (PUVA), nbUVB plus retinoid (Re-nbUVB), and PUVA plus retinoid (Re-PUVA), however, with rapid recurrence.

Authors+Show Affiliations

No affiliation info availableProf. Romana Čeović, MD, PhD, Department of Dermatovenereology University Hospital Center Zagreb, University of Zagreb School of Medicine , Šalata 4, 10000 Zagreb, Croatia; romana.ceovic@gmail.com.No affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info available

Pub Type(s)

Case Reports
Journal Article

Language

eng

PubMed ID

29782300

Citation

Jerković Gulin, Sandra, et al. "Poikilodermatous Mycosis Fungoides - Rare Entity, Different Treatment Modalities." Acta Dermatovenerologica Croatica : ADC, vol. 26, no. 1, 2018, pp. 48-52.
Jerković Gulin S, Čeović R, Ilić I, et al. Poikilodermatous Mycosis Fungoides - Rare Entity, Different Treatment Modalities. Acta Dermatovenerol Croat. 2018;26(1):48-52.
Jerković Gulin, S., Čeović, R., Ilić, I., Bradamante, M., Bukvić Mokos, Z., & Kostović, K. (2018). Poikilodermatous Mycosis Fungoides - Rare Entity, Different Treatment Modalities. Acta Dermatovenerologica Croatica : ADC, 26(1), 48-52.
Jerković Gulin S, et al. Poikilodermatous Mycosis Fungoides - Rare Entity, Different Treatment Modalities. Acta Dermatovenerol Croat. 2018;26(1):48-52. PubMed PMID: 29782300.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Poikilodermatous Mycosis Fungoides - Rare Entity, Different Treatment Modalities. AU - Jerković Gulin,Sandra, AU - Čeović,Romana, AU - Ilić,Ivana, AU - Bradamante,Mirna, AU - Bukvić Mokos,Zrinka, AU - Kostović,Krešimir, PY - 2018/5/22/entrez PY - 2018/5/22/pubmed PY - 2018/11/8/medline SP - 48 EP - 52 JF - Acta dermatovenerologica Croatica : ADC JO - Acta Dermatovenerol Croat VL - 26 IS - 1 N2 - Poikilodermatous mycosis fungoides (PMF) is a rare clinical variant of early-stage MF with peculiar histological features. Poikiloderma occurs in many different clinical conditions, which makes a diagnostic procedure more complicated. PMF belongs to a group of MF variants with low risk of disease progression. We report a case of a 64-year-old woman, who presented with mottled skin aspect of erythema, poikilodermatous patches (hypopigmentation, hyperpigmentation, atrophy, and telangiectasia) on more than 80% of the body. Based on clinical, histopathological, and immunohistochemical findings, we established the diagnosis of PMF. Staging procedure determined stage IIA. As skin-directed therapy was the treatment of choice, the patient was successfully treated with psoralen-UVA (PUVA), nbUVB plus retinoid (Re-nbUVB), and PUVA plus retinoid (Re-PUVA), however, with rapid recurrence. SN - 1847-6538 UR - https://www.unboundmedicine.com/medline/citation/29782300/Poikilodermatous_Mycosis_Fungoides___Rare_Entity_Different_Treatment_Modalities_ DB - PRIME DP - Unbound Medicine ER -