TY - JOUR T1 - Spinal anesthesia and postoperative epidural analgesia in a patient with congenital central hypoventilation syndrome -a case report. AU - Choi,Yongjoon, AU - Lee,Sunam, AU - Lee,Jiyeon, AU - Woo,Seongwon, Y1 - 2018/11/14/ PY - 2018/5/5/received PY - 2018/11/12/accepted PY - 2018/11/15/pubmed PY - 2020/7/17/medline PY - 2018/11/15/entrez KW - Autonomic dysregulation KW - Congenital central hypoventilation syndrome KW - Hypoxemia KW - Ondine’s curse KW - Spinal anesthesia SP - 375 EP - 380 JF - Korean journal of anesthesiology JO - Korean J Anesthesiol VL - 72 IS - 4 N2 - BACKGROUND: Congenital central hypoventilation syndrome (CCHS) is a rare disorder characterized by alveolar hypoventilation and autonomic dysregulation. Patients with CCHS have adequate ventilation while awake but exhibit hypoventilation while asleep. More severely affected patients exhibit hypoventilation both when awake and when asleep. CASE: Here, we report a case of successful spinal anesthesia and postoperative epidural analgesia in a patient with CCHS who underwent orthostatic surgery. CONCLUSIONS: In patients with CCHS, anesthesia is used with the goal of minimizing respiratory depression to avoid prolonged mechanical ventilation. Regional anesthesia should be considered where appropriate. Continuous oxygen saturation and end-tidal carbon dioxide monitoring must be available. SN - 2005-7563 UR - https://www.unboundmedicine.com/medline/citation/30424588/Spinal_anesthesia_and_postoperative_epidural_analgesia_in_a_patient_with_congenital_central_hypoventilation_syndrome__a_case_report_ DB - PRIME DP - Unbound Medicine ER -