Tags

Type your tag names separated by a space and hit enter

Hand Ischemia due to Steal Syndrome Associated with Multiple Arteriovenous Malformations in a Patient with Parkes-Weber Syndrome.
J Hand Surg Asian Pac Vol. 2019 Mar; 24(1):89-92.JH

Abstract

Parkes Weber Syndrome (PWS) is a congenital disorder characterized by the presence of arteriovenous malformations (AVMs) in upper or lower extremities. We herein present a 35 year-old male with PWS with complex AVMs in the right upper extremity; he had been previously treated with multiple sessions of vessel embolization, sclerotherapy and AVM resections. The patient presented to our clinic with two month history of progressive hand ischemia, digit necrosis and infection. Angiography was performed demonstrating numerous AVMs and filiform flow through the ulnar artery with poor opacification of arterial structures in the hand. Because of advanced ischemia, soft tissue infection and osteomyelitis, a distal forearm amputation was indicated. Hand threatening ischemia secondary to steal phenomenon associated to AVMs in PWS is rarely encountered and reported. This case illustrates a complex clinical presentation with advanced disease that required limb amputation.

Authors+Show Affiliations

* Department of Surgery, Mexico City, Mexico. ‖ Universidad Nacional Autonoma de Mexico, Mexico City, Mexico.† Section of Vascular Surgery and Endovascular Therapy, Mexico City, Mexico. ‖ Universidad Nacional Autonoma de Mexico, Mexico City, Mexico.‡ Departments of Radiology, Instituto Nacional de Ciencias Médicas y Nutrición Salvador Zubirán, Mexico City, Mexico. ‖ Universidad Nacional Autonoma de Mexico, Mexico City, Mexico.§ Departments of Pathology, Instituto Nacional de Ciencias Médicas y Nutrición Salvador Zubirán, Mexico City, Mexico. ‖ Universidad Nacional Autonoma de Mexico, Mexico City, Mexico.† Section of Vascular Surgery and Endovascular Therapy, Mexico City, Mexico. ‖ Universidad Nacional Autonoma de Mexico, Mexico City, Mexico.

Pub Type(s)

Case Reports
Journal Article

Language

eng

PubMed ID

30760156

Citation

Sánchez-Morales, Germán E., et al. "Hand Ischemia Due to Steal Syndrome Associated With Multiple Arteriovenous Malformations in a Patient With Parkes-Weber Syndrome." The Journal of Hand Surgery Asian-Pacific Volume, vol. 24, no. 1, 2019, pp. 89-92.
Sánchez-Morales GE, Anaya-Ayala JE, Serrano-Cueva MA, et al. Hand Ischemia due to Steal Syndrome Associated with Multiple Arteriovenous Malformations in a Patient with Parkes-Weber Syndrome. J Hand Surg Asian Pac Vol. 2019;24(1):89-92.
Sánchez-Morales, G. E., Anaya-Ayala, J. E., Serrano-Cueva, M. A., Salas-Torrez, E., & Hinojosa, C. A. (2019). Hand Ischemia due to Steal Syndrome Associated with Multiple Arteriovenous Malformations in a Patient with Parkes-Weber Syndrome. The Journal of Hand Surgery Asian-Pacific Volume, 24(1), 89-92. https://doi.org/10.1142/S2424835519720019
Sánchez-Morales GE, et al. Hand Ischemia Due to Steal Syndrome Associated With Multiple Arteriovenous Malformations in a Patient With Parkes-Weber Syndrome. J Hand Surg Asian Pac Vol. 2019;24(1):89-92. PubMed PMID: 30760156.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Hand Ischemia due to Steal Syndrome Associated with Multiple Arteriovenous Malformations in a Patient with Parkes-Weber Syndrome. AU - Sánchez-Morales,Germán E, AU - Anaya-Ayala,Javier E, AU - Serrano-Cueva,María A, AU - Salas-Torrez,Eladio, AU - Hinojosa,Carlos A, PY - 2019/2/15/entrez PY - 2019/2/15/pubmed PY - 2019/3/27/medline KW - Arteriovenous malformation KW - Hand ischemia KW - Parkes-Weber syndrome KW - Steal syndrome SP - 89 EP - 92 JF - The journal of hand surgery Asian-Pacific volume JO - J Hand Surg Asian Pac Vol VL - 24 IS - 1 N2 - Parkes Weber Syndrome (PWS) is a congenital disorder characterized by the presence of arteriovenous malformations (AVMs) in upper or lower extremities. We herein present a 35 year-old male with PWS with complex AVMs in the right upper extremity; he had been previously treated with multiple sessions of vessel embolization, sclerotherapy and AVM resections. The patient presented to our clinic with two month history of progressive hand ischemia, digit necrosis and infection. Angiography was performed demonstrating numerous AVMs and filiform flow through the ulnar artery with poor opacification of arterial structures in the hand. Because of advanced ischemia, soft tissue infection and osteomyelitis, a distal forearm amputation was indicated. Hand threatening ischemia secondary to steal phenomenon associated to AVMs in PWS is rarely encountered and reported. This case illustrates a complex clinical presentation with advanced disease that required limb amputation. SN - 2424-8363 UR - https://www.unboundmedicine.com/medline/citation/30760156/Hand_Ischemia_due_to_Steal_Syndrome_Associated_with_Multiple_Arteriovenous_Malformations_in_a_Patient_with_Parkes_Weber_Syndrome_ L2 - https://www.worldscientific.com/doi/full/10.1142/S2424835519720019?url_ver=Z39.88-2003&rfr_id=ori:rid:crossref.org&rfr_dat=cr_pub=pubmed DB - PRIME DP - Unbound Medicine ER -