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PRE AND POST-OPERATIVE OTORHINOLARYNGOLOGY SURGERY CARE IN PATIENTS WITH GLYCOGEN STORAGE DISEASE TYPE 1.

Abstract

OBJECTIVE

To discuss aspects of pre and post-operative otorhinolaryngology surgery in patients with glycogen storage disease type 1b.

CASE DESCRIPTION

Description of three clinical cases with probable glycogen storage disease type 1b who underwent otorhinolaryngology surgery, showing the importance of multidisciplinary interaction to avoid episodes of hypoglycemia.

COMMENTS

Patients with glycogen storage disease type 1b present recurrent infections, including the otorhinolaryngology affections. When there is an indication for surgical treatment, the caloric intake should be carefully followed in order to prevent hypoglycemia. The way to ensure this is to perform the pre and postoperative period in the hospital ward. In the postoperative period, it is important to make a slow transition between the intravenous and oral routes and not suspend the infusion of glucose during the surgical procedure. The cases illustrate the need for the interaction of the otorhinolaryngologic surgeon with the anesthesiologist, the pediatrician and the gastro-pediatrician in the management of these patients, avoiding hypoglycemic episodes.

Authors+Show Affiliations

Universidade Estadual de Campinas, São Paulo, SP, Brazil.Universidade Estadual de Campinas, São Paulo, SP, Brazil.Universidade Estadual de Campinas, São Paulo, SP, Brazil.Universidade Estadual de Campinas, São Paulo, SP, Brazil.Universidade Estadual de Campinas, São Paulo, SP, Brazil.

Pub Type(s)

Journal Article

Language

eng por

PubMed ID

31291441

Citation

Tommaso, Adriana Maria Alves de, et al. "PRE and POST-OPERATIVE OTORHINOLARYNGOLOGY SURGERY CARE in PATIENTS WITH GLYCOGEN STORAGE DISEASE TYPE 1." Revista Paulista De Pediatria : Orgao Oficial Da Sociedade De Pediatria De Sao Paulo, 2019.
Tommaso AMA, Hessel G, Riccetto AG, et al. PRE AND POST-OPERATIVE OTORHINOLARYNGOLOGY SURGERY CARE IN PATIENTS WITH GLYCOGEN STORAGE DISEASE TYPE 1. Rev Paul Pediatr. 2019.
Tommaso, A. M. A., Hessel, G., Riccetto, A. G., Semenzati, G. O., & Gusmão, R. J. (2019). PRE AND POST-OPERATIVE OTORHINOLARYNGOLOGY SURGERY CARE IN PATIENTS WITH GLYCOGEN STORAGE DISEASE TYPE 1. Revista Paulista De Pediatria : Orgao Oficial Da Sociedade De Pediatria De Sao Paulo, doi:10.1590/1984-0462/;2019;37;4;00005.
Tommaso AMA, et al. PRE and POST-OPERATIVE OTORHINOLARYNGOLOGY SURGERY CARE in PATIENTS WITH GLYCOGEN STORAGE DISEASE TYPE 1. Rev Paul Pediatr. 2019 Jul 4; PubMed PMID: 31291441.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - PRE AND POST-OPERATIVE OTORHINOLARYNGOLOGY SURGERY CARE IN PATIENTS WITH GLYCOGEN STORAGE DISEASE TYPE 1. AU - Tommaso,Adriana Maria Alves de, AU - Hessel,Gabriel, AU - Riccetto,Adriana Gut, AU - Semenzati,Graziela de Oliveira, AU - Gusmão,Reinaldo Jordão, Y1 - 2019/07/04/ PY - 2017/12/10/received PY - 2018/04/29/accepted PY - 2019/7/11/entrez JF - Revista paulista de pediatria : orgao oficial da Sociedade de Pediatria de Sao Paulo JO - Rev Paul Pediatr N2 - OBJECTIVE: To discuss aspects of pre and post-operative otorhinolaryngology surgery in patients with glycogen storage disease type 1b. CASE DESCRIPTION: Description of three clinical cases with probable glycogen storage disease type 1b who underwent otorhinolaryngology surgery, showing the importance of multidisciplinary interaction to avoid episodes of hypoglycemia. COMMENTS: Patients with glycogen storage disease type 1b present recurrent infections, including the otorhinolaryngology affections. When there is an indication for surgical treatment, the caloric intake should be carefully followed in order to prevent hypoglycemia. The way to ensure this is to perform the pre and postoperative period in the hospital ward. In the postoperative period, it is important to make a slow transition between the intravenous and oral routes and not suspend the infusion of glucose during the surgical procedure. The cases illustrate the need for the interaction of the otorhinolaryngologic surgeon with the anesthesiologist, the pediatrician and the gastro-pediatrician in the management of these patients, avoiding hypoglycemic episodes. SN - 1984-0462 UR - https://www.unboundmedicine.com/medline/citation/31291441/PRE_AND_POST-OPERATIVE_OTORHINOLARYNGOLOGY_SURGERY_CARE_IN_PATIENTS_WITH_GLYCOGEN_STORAGE_DISEASE_TYPE_1 L2 - https://linkinghub.elsevier.com/retrieve/pii/S0103-05822019005013102 DB - PRIME DP - Unbound Medicine ER -