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L-looped Transposition of the Great Arteries in a Patient with Marfanoid Habitus: First Reported Case in Literature.
Cureus 2019; 11(8):e5416C

Abstract

L-looped transposition of great arteries (L-TGA) is an extremely rare heart condition. It is associated with physiologically corrected transposition of great vessels, leading to the normal return of deoxygenated systemic venous blood to the heart and transport of oxygenated pulmonary venous blood to the main systemic circulation. Anatomic discordancy and anomalous coronary artery distribution predispose the right ventricle to excessive workload and eventual heart failure. This mandates anatomic correction or proper medical management of heart failure. Herein, we present a case of a 14-year-old girl who presented to our cardiology consults with a false impression of pre-made clinical diagnosis of tetralogy of Fallot. She had increasing dyspnea and cyanosis on presentation. Striking marfanoid habitus and unusual echocardiographic findings of tripartite geometry of heart with parallel and discordant positioning of atria, ventricles, and great arteries led us to cardiac computed tomography which confirmed the diagnosis of L-TGA. Our patient also had associated patent ductus arteriosus, dextrocardia, ventricular septal defect (VSD), and pulmonary atresia. Due to the complex nature of heart disease and unavailability of resources, she was treated with a comprehensive heart failure protocol and followed up clinically and radiologically at regular intervals and showed massive improvement. This is the first-ever documented case of L-TGA with complex shunting and marfanoid habitus.

Authors+Show Affiliations

Cardiology, Civil Hospital Karachi, Dow University of Health Sciences, Karachi, PAK.Internal Medicine, Civil Hospital Karachi, Dow University of Health Sciences, Karachi, PAK.Cardiology, Civil Hospital Karachi, Dow University of Health Sciences, Karachi, PAK.Internal Medicine, Dow University of Health Sciences, Karachi, PAK.Internal Medicine, Dow University of Health Sciences, Karachi, PAK.

Pub Type(s)

Case Reports

Language

eng

PubMed ID

31632869

Citation

Majid, Abdul, et al. "L-looped Transposition of the Great Arteries in a Patient With Marfanoid Habitus: First Reported Case in Literature." Cureus, vol. 11, no. 8, 2019, pp. e5416.
Majid A, Bin Waqar SH, Yasmin F, et al. L-looped Transposition of the Great Arteries in a Patient with Marfanoid Habitus: First Reported Case in Literature. Cureus. 2019;11(8):e5416.
Majid, A., Bin Waqar, S. H., Yasmin, F., Mohiuddin, O., & Khan, A. A. (2019). L-looped Transposition of the Great Arteries in a Patient with Marfanoid Habitus: First Reported Case in Literature. Cureus, 11(8), pp. e5416. doi:10.7759/cureus.5416.
Majid A, et al. L-looped Transposition of the Great Arteries in a Patient With Marfanoid Habitus: First Reported Case in Literature. Cureus. 2019 Aug 18;11(8):e5416. PubMed PMID: 31632869.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - L-looped Transposition of the Great Arteries in a Patient with Marfanoid Habitus: First Reported Case in Literature. AU - Majid,Abdul, AU - Bin Waqar,Syed Hamza, AU - Yasmin,Farah, AU - Mohiuddin,Osama, AU - Khan,Anosh Aslam, Y1 - 2019/08/18/ PY - 2019/10/22/entrez PY - 2019/10/22/pubmed PY - 2019/10/22/medline KW - atrial-switch KW - dextrocardia KW - discordancy KW - l-tga KW - marfanoid KW - pda KW - transposition of great arteries KW - vsd SP - e5416 EP - e5416 JF - Cureus JO - Cureus VL - 11 IS - 8 N2 - L-looped transposition of great arteries (L-TGA) is an extremely rare heart condition. It is associated with physiologically corrected transposition of great vessels, leading to the normal return of deoxygenated systemic venous blood to the heart and transport of oxygenated pulmonary venous blood to the main systemic circulation. Anatomic discordancy and anomalous coronary artery distribution predispose the right ventricle to excessive workload and eventual heart failure. This mandates anatomic correction or proper medical management of heart failure. Herein, we present a case of a 14-year-old girl who presented to our cardiology consults with a false impression of pre-made clinical diagnosis of tetralogy of Fallot. She had increasing dyspnea and cyanosis on presentation. Striking marfanoid habitus and unusual echocardiographic findings of tripartite geometry of heart with parallel and discordant positioning of atria, ventricles, and great arteries led us to cardiac computed tomography which confirmed the diagnosis of L-TGA. Our patient also had associated patent ductus arteriosus, dextrocardia, ventricular septal defect (VSD), and pulmonary atresia. Due to the complex nature of heart disease and unavailability of resources, she was treated with a comprehensive heart failure protocol and followed up clinically and radiologically at regular intervals and showed massive improvement. This is the first-ever documented case of L-TGA with complex shunting and marfanoid habitus. SN - 2168-8184 UR - https://www.unboundmedicine.com/medline/citation/31632869/L-looped_Transposition_of_the_Great_Arteries_in_a_Patient_with_Marfanoid_Habitus:_First_Reported_Case_in_Literature L2 - https://www.ncbi.nlm.nih.gov/pmc/articles/pmid/31632869/ DB - PRIME DP - Unbound Medicine ER -