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Lipofibromatosis-Like Neural Tumor: A Case Report and Review of the Literature.
Am J Dermatopathol. 2020 Jun 30 [Online ahead of print]AJ

Abstract

Lipofibromatosis-like neural tumors (LPF-NT) are soft tissue tumors characterized by a lipofibromatosis-like pattern, CD34/PS100 positivity, and recurrent NTRK1 gene rearrangement. It occurs mainly in pediatric patients or young adults. We report here, the first case of LPF-NT in a middle-aged adult initially misdiagnosed as a myoepithelial tumor. LPF-NT may have a locally aggressive course but no recurrence was seen after complete surgeries, whereas metastatic diseases remain exceptional.

Authors+Show Affiliations

Hospices Civils de Lyon, Hôpital Lyon Sud, Service d'anatomie et de cytologie pathologiques, Pierre Bénite, France.Hospices Civils de Lyon, Hôpital Lyon Sud, Service de biochimie et de biologie moléculaire, Pierre Bénite, France.Hospices Civils de Lyon, Groupement hospitalier Est, Service de biologie moléculaire, Bron, France.Hospices Civils de Lyon, Hôpital Lyon Sud, Service de dermatologie, Pierre Bénite, France.Hospices Civils de Lyon, Hôpital Lyon Sud, Service d'anatomie et de cytologie pathologiques, Pierre Bénite, France.Hospices Civils de Lyon, Hôpital Lyon Sud, Service d'anatomie et de cytologie pathologiques, Pierre Bénite, France.Hospices Civils de Lyon, Hôpital Lyon Sud, Service de biochimie et de biologie moléculaire, Pierre Bénite, France. Cancer Research Center of Lyon, INSERM1052, CNRS5286, Université de Lyon, Lyon, France.Hospices Civils de Lyon, Hôpital Lyon Sud, Service d'anatomie et de cytologie pathologiques, Pierre Bénite, France.

Pub Type(s)

Journal Article

Language

eng

PubMed ID

32618702

Citation

Crumbach, Laura, et al. "Lipofibromatosis-Like Neural Tumor: a Case Report and Review of the Literature." The American Journal of Dermatopathology, 2020.
Crumbach L, Descotes F, Bringuier PP, et al. Lipofibromatosis-Like Neural Tumor: A Case Report and Review of the Literature. Am J Dermatopathol. 2020.
Crumbach, L., Descotes, F., Bringuier, P. P., Poulalhon, N., Balme, B., Juliet, T., Lopez, J., & Harou, O. (2020). Lipofibromatosis-Like Neural Tumor: A Case Report and Review of the Literature. The American Journal of Dermatopathology. https://doi.org/10.1097/DAD.0000000000001734
Crumbach L, et al. Lipofibromatosis-Like Neural Tumor: a Case Report and Review of the Literature. Am J Dermatopathol. 2020 Jun 30; PubMed PMID: 32618702.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Lipofibromatosis-Like Neural Tumor: A Case Report and Review of the Literature. AU - Crumbach,Laura, AU - Descotes,Françoise, AU - Bringuier,Pierre-Paul, AU - Poulalhon,Nicolas, AU - Balme,Brigitte, AU - Juliet,Tantot, AU - Lopez,Jonathan, AU - Harou,Olivier, Y1 - 2020/06/30/ PY - 2020/7/4/entrez JF - The American Journal of dermatopathology JO - Am J Dermatopathol N2 - Lipofibromatosis-like neural tumors (LPF-NT) are soft tissue tumors characterized by a lipofibromatosis-like pattern, CD34/PS100 positivity, and recurrent NTRK1 gene rearrangement. It occurs mainly in pediatric patients or young adults. We report here, the first case of LPF-NT in a middle-aged adult initially misdiagnosed as a myoepithelial tumor. LPF-NT may have a locally aggressive course but no recurrence was seen after complete surgeries, whereas metastatic diseases remain exceptional. SN - 1533-0311 UR - https://www.unboundmedicine.com/medline/citation/32618702/Lipofibromatosis-Like_Neural_Tumor:_A_Case_Report_and_Review_of_the_Literature L2 - https://doi.org/10.1097/DAD.0000000000001734 DB - PRIME DP - Unbound Medicine ER -