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Myotonic dystrophy: ambulatory electrocardiogram, electrophysiologic study, and echocardiographic evaluation.
Am Heart J. 1987 Jun; 113(6):1482-8.AH

Abstract

Myotonic dystrophy is frequently associated with functional and anatomic derangements in the myocardium. Ten myotonic dystrophy patients (seven men and three women, ages ranging from 35 to 58 years) were evaluated with a 12-lead ECG, 24-hour Holter monitor recording, invasive electrophysiologic studies, and echocardiographic examination. Nine patients displayed abnormalities in the conduction system. ECG and Holter monitor abnormalities were first-degree atrioventricular block (n = 8), second-degree atrioventricular block (n = 1) (Wenckebach type), complete left bundle branch block (n = 2), left anterior fascicular block (n = 5), left posterior fascicular block (n = 1), sinus bradycardia (n = 6), sick sinus syndrome (n = 2), frequent premature ventricular complexes (n = 4), and ventricular tachycardia (n = 2). Electrophysiologic study abnormalities included AH interval less than or equal to 140 msec (n = 7), AH interval greater than 140 msec (n = 3), HV interval greater than 60 msec (n = 9), and ventricular tachycardia induction (n = 1). Echocardiographic examination revealed mitral valve prolapse (n = 6). We conclude that diffuse conduction abnormalities were seen in a majority of our patients with myotonic dystrophy. Ventricular arrhythmias, including ventricular tachycardia, were seen in some of these patients, and mitral valve prolapse was a frequent finding.

Authors

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Pub Type(s)

Journal Article

Language

eng

PubMed ID

3591615

Citation

Hiromasa, S, et al. "Myotonic Dystrophy: Ambulatory Electrocardiogram, Electrophysiologic Study, and Echocardiographic Evaluation." American Heart Journal, vol. 113, no. 6, 1987, pp. 1482-8.
Hiromasa S, Ikeda T, Kubota K, et al. Myotonic dystrophy: ambulatory electrocardiogram, electrophysiologic study, and echocardiographic evaluation. Am Heart J. 1987;113(6):1482-8.
Hiromasa, S., Ikeda, T., Kubota, K., Hattori, N., Nishimura, M., Watanabe, Y., Maldonado, C., Palakurthy, P. R., & Kupersmith, J. (1987). Myotonic dystrophy: ambulatory electrocardiogram, electrophysiologic study, and echocardiographic evaluation. American Heart Journal, 113(6), 1482-8.
Hiromasa S, et al. Myotonic Dystrophy: Ambulatory Electrocardiogram, Electrophysiologic Study, and Echocardiographic Evaluation. Am Heart J. 1987;113(6):1482-8. PubMed PMID: 3591615.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Myotonic dystrophy: ambulatory electrocardiogram, electrophysiologic study, and echocardiographic evaluation. AU - Hiromasa,S, AU - Ikeda,T, AU - Kubota,K, AU - Hattori,N, AU - Nishimura,M, AU - Watanabe,Y, AU - Maldonado,C, AU - Palakurthy,P R, AU - Kupersmith,J, PY - 1987/6/1/pubmed PY - 1987/6/1/medline PY - 1987/6/1/entrez SP - 1482 EP - 8 JF - American heart journal JO - Am. Heart J. VL - 113 IS - 6 N2 - Myotonic dystrophy is frequently associated with functional and anatomic derangements in the myocardium. Ten myotonic dystrophy patients (seven men and three women, ages ranging from 35 to 58 years) were evaluated with a 12-lead ECG, 24-hour Holter monitor recording, invasive electrophysiologic studies, and echocardiographic examination. Nine patients displayed abnormalities in the conduction system. ECG and Holter monitor abnormalities were first-degree atrioventricular block (n = 8), second-degree atrioventricular block (n = 1) (Wenckebach type), complete left bundle branch block (n = 2), left anterior fascicular block (n = 5), left posterior fascicular block (n = 1), sinus bradycardia (n = 6), sick sinus syndrome (n = 2), frequent premature ventricular complexes (n = 4), and ventricular tachycardia (n = 2). Electrophysiologic study abnormalities included AH interval less than or equal to 140 msec (n = 7), AH interval greater than 140 msec (n = 3), HV interval greater than 60 msec (n = 9), and ventricular tachycardia induction (n = 1). Echocardiographic examination revealed mitral valve prolapse (n = 6). We conclude that diffuse conduction abnormalities were seen in a majority of our patients with myotonic dystrophy. Ventricular arrhythmias, including ventricular tachycardia, were seen in some of these patients, and mitral valve prolapse was a frequent finding. SN - 0002-8703 UR - https://www.unboundmedicine.com/medline/citation/3591615/Myotonic_dystrophy:_ambulatory_electrocardiogram_electrophysiologic_study_and_echocardiographic_evaluation_ L2 - https://linkinghub.elsevier.com/retrieve/pii/0002-8703(87)90665-X DB - PRIME DP - Unbound Medicine ER -