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Prenatal diagnosis of Dandy-Walker malformation: report of a case.
J Formos Med Assoc. 1994 Nov-Dec; 93(11-12):967-70.JF

Abstract

Dandy-Walker malformation is one of the major causes of congenital hydrocephalus. We report on a case that was diagnosed by sonography in a fetus at 34 weeks' gestation. The diagnosis was confirmed by postnatal computed tomographic (CT) brain scan and magnetic resonance imaging (MRI). The prenatal sonographic findings were a large posterior fossa in communication with the fourth ventricle, a small and splayed cerebellar hemisphere and marked degrees of ventriculomegaly. The postnatal CT scan images were similar to the prenatal sonography. The hypoplasia of the cerebellar vermis and the associated hypogenesis of the corpus callosum can only be clearly delineated by MRI. Dandy-Walker malformation is one form of the Dandy-Walker complex and cystic malformations of the posterior fossa. It should be differentiated from Dandy-Walker variant, or mega-cisterna magna, and arachnoid cyst. Dandy-Walker complex may be associated with chromosomal, intracranial and extracranial abnormalities. Early in utero detection is useful for detailed evaluation of associated anomalies. Obstetric management depends on gestational age, karyotype abnormality and associated intracranial and extracranial anomalies. In the present report, the infant presented no progressive ventriculomegaly and no surgery was required. The infant developed normally.

Authors+Show Affiliations

Department of Obstetrics and Gynecology, Keelung Chang Gung Memorial Hospital, Taiwan R.O.C.No affiliation info available

Pub Type(s)

Case Reports
Journal Article

Language

eng

PubMed ID

7633204

Citation

Chen, F P., and K K. Chu. "Prenatal Diagnosis of Dandy-Walker Malformation: Report of a Case." Journal of the Formosan Medical Association = Taiwan Yi Zhi, vol. 93, no. 11-12, 1994, pp. 967-70.
Chen FP, Chu KK. Prenatal diagnosis of Dandy-Walker malformation: report of a case. J Formos Med Assoc. 1994;93(11-12):967-70.
Chen, F. P., & Chu, K. K. (1994). Prenatal diagnosis of Dandy-Walker malformation: report of a case. Journal of the Formosan Medical Association = Taiwan Yi Zhi, 93(11-12), 967-70.
Chen FP, Chu KK. Prenatal Diagnosis of Dandy-Walker Malformation: Report of a Case. J Formos Med Assoc. 1994 Nov-Dec;93(11-12):967-70. PubMed PMID: 7633204.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Prenatal diagnosis of Dandy-Walker malformation: report of a case. AU - Chen,F P, AU - Chu,K K, PY - 1994/11/1/pubmed PY - 1994/11/1/medline PY - 1994/11/1/entrez SP - 967 EP - 70 JF - Journal of the Formosan Medical Association = Taiwan yi zhi JO - J Formos Med Assoc VL - 93 IS - 11-12 N2 - Dandy-Walker malformation is one of the major causes of congenital hydrocephalus. We report on a case that was diagnosed by sonography in a fetus at 34 weeks' gestation. The diagnosis was confirmed by postnatal computed tomographic (CT) brain scan and magnetic resonance imaging (MRI). The prenatal sonographic findings were a large posterior fossa in communication with the fourth ventricle, a small and splayed cerebellar hemisphere and marked degrees of ventriculomegaly. The postnatal CT scan images were similar to the prenatal sonography. The hypoplasia of the cerebellar vermis and the associated hypogenesis of the corpus callosum can only be clearly delineated by MRI. Dandy-Walker malformation is one form of the Dandy-Walker complex and cystic malformations of the posterior fossa. It should be differentiated from Dandy-Walker variant, or mega-cisterna magna, and arachnoid cyst. Dandy-Walker complex may be associated with chromosomal, intracranial and extracranial abnormalities. Early in utero detection is useful for detailed evaluation of associated anomalies. Obstetric management depends on gestational age, karyotype abnormality and associated intracranial and extracranial anomalies. In the present report, the infant presented no progressive ventriculomegaly and no surgery was required. The infant developed normally. SN - 0929-6646 UR - https://www.unboundmedicine.com/medline/citation/7633204/Prenatal_diagnosis_of_Dandy_Walker_malformation:_report_of_a_case_ L2 - https://medlineplus.gov/fetalhealthanddevelopment.html DB - PRIME DP - Unbound Medicine ER -