Tags

Type your tag names separated by a space and hit enter

Progressive systemic sclerosis sine scleroderma in a child presenting as nocturnal seizures and Raynaud's phenomenon.
Acta Paediatr. 1993 Jan; 82(1):122-3.AP

Abstract

Progressive systemic sclerosis sine scleroderma, as well as neurological manifestations of progressive systemic sclerosis are rare in adult-onset cases. Neither have been reported in children with progressive systemic sclerosis, either separately or together. We describe a six-year-old girl with nocturnal seizures and Raynaud's phenomenon of three years' duration. She died of cardiopulmonary sclerosis without ever fitting the required criteria of systemic sclerosis. Nailfold capillaroscopy revealed the specific "scleroderma-pattern" and provided the only clue for a diagnosis of progressive systemic sclerosis, confirmed eventually by skin biopsy.

Authors+Show Affiliations

Department of Pediatrics, Bikur Cholim General Hospital, Jerusalem, Israel.No affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info available

Pub Type(s)

Case Reports
Journal Article

Language

eng

PubMed ID

8453211

Citation

Navon, P, et al. "Progressive Systemic Sclerosis Sine Scleroderma in a Child Presenting as Nocturnal Seizures and Raynaud's Phenomenon." Acta Paediatrica (Oslo, Norway : 1992), vol. 82, no. 1, 1993, pp. 122-3.
Navon P, Halevi A, Brand A, et al. Progressive systemic sclerosis sine scleroderma in a child presenting as nocturnal seizures and Raynaud's phenomenon. Acta Paediatr. 1993;82(1):122-3.
Navon, P., Halevi, A., Brand, A., Branski, D., & Rubinow, A. (1993). Progressive systemic sclerosis sine scleroderma in a child presenting as nocturnal seizures and Raynaud's phenomenon. Acta Paediatrica (Oslo, Norway : 1992), 82(1), 122-3.
Navon P, et al. Progressive Systemic Sclerosis Sine Scleroderma in a Child Presenting as Nocturnal Seizures and Raynaud's Phenomenon. Acta Paediatr. 1993;82(1):122-3. PubMed PMID: 8453211.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Progressive systemic sclerosis sine scleroderma in a child presenting as nocturnal seizures and Raynaud's phenomenon. AU - Navon,P, AU - Halevi,A, AU - Brand,A, AU - Branski,D, AU - Rubinow,A, PY - 1993/1/1/pubmed PY - 1993/1/1/medline PY - 1993/1/1/entrez SP - 122 EP - 3 JF - Acta paediatrica (Oslo, Norway : 1992) JO - Acta Paediatr. VL - 82 IS - 1 N2 - Progressive systemic sclerosis sine scleroderma, as well as neurological manifestations of progressive systemic sclerosis are rare in adult-onset cases. Neither have been reported in children with progressive systemic sclerosis, either separately or together. We describe a six-year-old girl with nocturnal seizures and Raynaud's phenomenon of three years' duration. She died of cardiopulmonary sclerosis without ever fitting the required criteria of systemic sclerosis. Nailfold capillaroscopy revealed the specific "scleroderma-pattern" and provided the only clue for a diagnosis of progressive systemic sclerosis, confirmed eventually by skin biopsy. SN - 0803-5253 UR - https://www.unboundmedicine.com/medline/citation/8453211/Progressive_systemic_sclerosis_sine_scleroderma_in_a_child_presenting_as_nocturnal_seizures_and_Raynaud's_phenomenon_ L2 - https://onlinelibrary.wiley.com/resolve/openurl?genre=article&sid=nlm:pubmed&issn=0803-5253&date=1993&volume=82&issue=1&spage=122 DB - PRIME DP - Unbound Medicine ER -