Tags

Type your tag names separated by a space and hit enter

Primary intramedullary spinal cord primitive neuroectodermal tumor with intracranial seeding in an infant.
Childs Nerv Syst. 1996 Oct; 12(10):633-6.CN

Abstract

Primary spinal cord primitive neuroectodermal tumor (PNET) is a rare entity. In all 13 cases have been reported in the literature, including 3 with intracranial seeding. A 3-month-old girl with involvement of the spinal cord below the mid-thoracic level is described. The brain MRI revealed findings indicative of seeding along the intracranial subarachnoid space. Biopsy, duraplasty and removal of laminotomy flap were done. In spite of a good response to the first cycle of postoperative "8-drugs-in-a-day' chemotherapy, further treatment was refused. She died 21 days after the onset of leg weakness, which reveals the rapid progression of untreated cases. To our knowledge, this is the first case of spinal cord PNET with parenchymal involvement that has been described in an infant.

Authors+Show Affiliations

Division of Pediatric Neurosurgery, Seoul National University Children's Hospital, Yongon-dong, Chongno-gu, Korea.No affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info available

Pub Type(s)

Case Reports
Journal Article

Language

eng

PubMed ID

8934026

Citation

Kwon, O K., et al. "Primary Intramedullary Spinal Cord Primitive Neuroectodermal Tumor With Intracranial Seeding in an Infant." Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery, vol. 12, no. 10, 1996, pp. 633-6.
Kwon OK, Wang KC, Kim CJ, et al. Primary intramedullary spinal cord primitive neuroectodermal tumor with intracranial seeding in an infant. Childs Nerv Syst. 1996;12(10):633-6.
Kwon, O. K., Wang, K. C., Kim, C. J., Kim, I. O., Chi, J. G., & Cho, B. K. (1996). Primary intramedullary spinal cord primitive neuroectodermal tumor with intracranial seeding in an infant. Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery, 12(10), 633-6.
Kwon OK, et al. Primary Intramedullary Spinal Cord Primitive Neuroectodermal Tumor With Intracranial Seeding in an Infant. Childs Nerv Syst. 1996;12(10):633-6. PubMed PMID: 8934026.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Primary intramedullary spinal cord primitive neuroectodermal tumor with intracranial seeding in an infant. AU - Kwon,O K, AU - Wang,K C, AU - Kim,C J, AU - Kim,I O, AU - Chi,J G, AU - Cho,B K, PY - 1996/10/1/pubmed PY - 1996/10/1/medline PY - 1996/10/1/entrez SP - 633 EP - 6 JF - Child's nervous system : ChNS : official journal of the International Society for Pediatric Neurosurgery JO - Childs Nerv Syst VL - 12 IS - 10 N2 - Primary spinal cord primitive neuroectodermal tumor (PNET) is a rare entity. In all 13 cases have been reported in the literature, including 3 with intracranial seeding. A 3-month-old girl with involvement of the spinal cord below the mid-thoracic level is described. The brain MRI revealed findings indicative of seeding along the intracranial subarachnoid space. Biopsy, duraplasty and removal of laminotomy flap were done. In spite of a good response to the first cycle of postoperative "8-drugs-in-a-day' chemotherapy, further treatment was refused. She died 21 days after the onset of leg weakness, which reveals the rapid progression of untreated cases. To our knowledge, this is the first case of spinal cord PNET with parenchymal involvement that has been described in an infant. SN - 0256-7040 UR - https://www.unboundmedicine.com/medline/citation/8934026/Primary_intramedullary_spinal_cord_primitive_neuroectodermal_tumor_with_intracranial_seeding_in_an_infant_ L2 - https://doi.org/10.1007/bf00261661 DB - PRIME DP - Unbound Medicine ER -