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Pierre Robin syndrome: characteristics of hearing loss, effect of age on hearing level and possibilities in therapy planning.
J Laryngol Otol. 1996 Sep; 110(9):830-5.JL

Abstract

Hearing loss was studied in 22 patients with Pierre Robin syndrome (PRS) aged three to 12 years (median 5.0 years). The results were compared to those obtained in 62 patients with isolated cleft palate (ICP) aged one to 27 years (median 5.5 years). Hearing loss was more frequently found in PRS (73.3 per cent) than in ICP (58.1 per cent) patients (p = 0.02). PRS patients had more ears with moderate (21-40 dB) and severe (> 40 dB) hearing loss, disturbing their social contact, with no tendency to normalization with age (Spearman r = 0.065). In contrast to PRS, ICP patients showed a significant tendency to hearing level normalization with ageing (Spearman r = -0.453; p = 0.001). Planigraphs of temporal bones showed inadequately developed pneumatization of the mastoid bone in all PRS patients and in most ICP patients. No malformation of the inner or middle ear was found in either group. PRS patients have a significantly higher risk of conductive hearing loss than those with ICP. Use of tympanostomy (ventilation) tubes is therapy of choice in patients with Pierre Robin syndrome, and it should be introduced as early as possible, even at the same time as palatoplasty.

Authors+Show Affiliations

Department of Otolaryngology, Zagreb University Clinical Hospital Centre Salata, Croatia.No affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info availableNo affiliation info available

Pub Type(s)

Comparative Study
Journal Article

Language

eng

PubMed ID

8949291

Citation

Handzić-Cuk, J, et al. "Pierre Robin Syndrome: Characteristics of Hearing Loss, Effect of Age On Hearing Level and Possibilities in Therapy Planning." The Journal of Laryngology and Otology, vol. 110, no. 9, 1996, pp. 830-5.
Handzić-Cuk J, Cuk V, Risavi R, et al. Pierre Robin syndrome: characteristics of hearing loss, effect of age on hearing level and possibilities in therapy planning. J Laryngol Otol. 1996;110(9):830-5.
Handzić-Cuk, J., Cuk, V., Risavi, R., Katić, V., Katusić, D., Bagatin, M., Stajner-Katusić, S., & Gortan, D. (1996). Pierre Robin syndrome: characteristics of hearing loss, effect of age on hearing level and possibilities in therapy planning. The Journal of Laryngology and Otology, 110(9), 830-5.
Handzić-Cuk J, et al. Pierre Robin Syndrome: Characteristics of Hearing Loss, Effect of Age On Hearing Level and Possibilities in Therapy Planning. J Laryngol Otol. 1996;110(9):830-5. PubMed PMID: 8949291.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - Pierre Robin syndrome: characteristics of hearing loss, effect of age on hearing level and possibilities in therapy planning. AU - Handzić-Cuk,J, AU - Cuk,V, AU - Risavi,R, AU - Katić,V, AU - Katusić,D, AU - Bagatin,M, AU - Stajner-Katusić,S, AU - Gortan,D, PY - 1996/9/1/pubmed PY - 1996/9/1/medline PY - 1996/9/1/entrez SP - 830 EP - 5 JF - The Journal of laryngology and otology JO - J Laryngol Otol VL - 110 IS - 9 N2 - Hearing loss was studied in 22 patients with Pierre Robin syndrome (PRS) aged three to 12 years (median 5.0 years). The results were compared to those obtained in 62 patients with isolated cleft palate (ICP) aged one to 27 years (median 5.5 years). Hearing loss was more frequently found in PRS (73.3 per cent) than in ICP (58.1 per cent) patients (p = 0.02). PRS patients had more ears with moderate (21-40 dB) and severe (> 40 dB) hearing loss, disturbing their social contact, with no tendency to normalization with age (Spearman r = 0.065). In contrast to PRS, ICP patients showed a significant tendency to hearing level normalization with ageing (Spearman r = -0.453; p = 0.001). Planigraphs of temporal bones showed inadequately developed pneumatization of the mastoid bone in all PRS patients and in most ICP patients. No malformation of the inner or middle ear was found in either group. PRS patients have a significantly higher risk of conductive hearing loss than those with ICP. Use of tympanostomy (ventilation) tubes is therapy of choice in patients with Pierre Robin syndrome, and it should be introduced as early as possible, even at the same time as palatoplasty. SN - 0022-2151 UR - https://www.unboundmedicine.com/medline/citation/8949291/Pierre_Robin_syndrome:_characteristics_of_hearing_loss_effect_of_age_on_hearing_level_and_possibilities_in_therapy_planning_ L2 - https://medlineplus.gov/olderadulthealth.html DB - PRIME DP - Unbound Medicine ER -