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[Idiopathic portal hypertension, multiple focal nodular hepatic hyperplasia, the CREST syndrome and protein S deficiency].
Rev Esp Enferm Dig. 1997 Jan; 89(1):55-9.RE

Abstract

A 54 year old woman with idiopathic portal hypertension, CREST syndrome, protein "S" deficiency and multiple focal nodular hyperplasia is reported. The patient presented several episodes of upper digestive bleeding due to portal hypertension gastropathy and to esophageal varices. Treatment with propanolol and isosorbide 5-mononitrate failed to control recurrent bleeding and a portacaval shunt was performed. At operation, ten hepatic nodes were found, being diagnosed as focal nodular hyperplasia in the pathologic study. Congestive gastropathy, esophageal varices and splenomegaly disappeared after portacaval shunt and bleeding did not recur after a follow-up of twelve months. This results support the role of portal decompressive surgery in the bleeding due to portal hypertension gastropathy.

Authors+Show Affiliations

Sánchez Manuel J
Servicio de Cirugía General, Hospital General Yagüe, Burgos.
Seco Gil JL
No affiliation info available
Saez-Royuela F
No affiliation info available
Llanos Chávarri MC
No affiliation info available
Pérez Alvarez JC
No affiliation info available
García Plata E
No affiliation info available
López Morante A
No affiliation info available

MeSH

BiopsyCREST SyndromeFemaleGastrointestinal HemorrhageHumansHyperplasiaHypertension, PortalLiverMiddle AgedProtein S Deficiency

Pub Type(s)

Case Reports
English Abstract
Journal Article
Review

Language

spa

PubMed ID

9090984

Citation

Sánchez Manuel, J, et al. "[Idiopathic Portal Hypertension, Multiple Focal Nodular Hepatic Hyperplasia, the CREST Syndrome and Protein S Deficiency]." Revista Espanola De Enfermedades Digestivas : Organo Oficial De La Sociedad Espanola De Patologia Digestiva, vol. 89, no. 1, 1997, pp. 55-9.
Sánchez Manuel J, Seco Gil JL, Saez-Royuela F, et al. [Idiopathic portal hypertension, multiple focal nodular hepatic hyperplasia, the CREST syndrome and protein S deficiency]. Rev Esp Enferm Dig. 1997;89(1):55-9.
Sánchez Manuel, J., Seco Gil, J. L., Saez-Royuela, F., Llanos Chávarri, M. C., Pérez Alvarez, J. C., García Plata, E., & López Morante, A. (1997). [Idiopathic portal hypertension, multiple focal nodular hepatic hyperplasia, the CREST syndrome and protein S deficiency]. Revista Espanola De Enfermedades Digestivas : Organo Oficial De La Sociedad Espanola De Patologia Digestiva, 89(1), 55-9.
Sánchez Manuel J, et al. [Idiopathic Portal Hypertension, Multiple Focal Nodular Hepatic Hyperplasia, the CREST Syndrome and Protein S Deficiency]. Rev Esp Enferm Dig. 1997;89(1):55-9. PubMed PMID: 9090984.
* Article titles in AMA citation format should be in sentence-case
TY - JOUR T1 - [Idiopathic portal hypertension, multiple focal nodular hepatic hyperplasia, the CREST syndrome and protein S deficiency]. AU - Sánchez Manuel,J, AU - Seco Gil,J L, AU - Saez-Royuela,F, AU - Llanos Chávarri,M C, AU - Pérez Alvarez,J C, AU - García Plata,E, AU - López Morante,A, PY - 1997/1/1/pubmed PY - 1997/1/1/medline PY - 1997/1/1/entrez SP - 55 EP - 9 JF - Revista espanola de enfermedades digestivas : organo oficial de la Sociedad Espanola de Patologia Digestiva JO - Rev Esp Enferm Dig VL - 89 IS - 1 N2 - A 54 year old woman with idiopathic portal hypertension, CREST syndrome, protein "S" deficiency and multiple focal nodular hyperplasia is reported. The patient presented several episodes of upper digestive bleeding due to portal hypertension gastropathy and to esophageal varices. Treatment with propanolol and isosorbide 5-mononitrate failed to control recurrent bleeding and a portacaval shunt was performed. At operation, ten hepatic nodes were found, being diagnosed as focal nodular hyperplasia in the pathologic study. Congestive gastropathy, esophageal varices and splenomegaly disappeared after portacaval shunt and bleeding did not recur after a follow-up of twelve months. This results support the role of portal decompressive surgery in the bleeding due to portal hypertension gastropathy. SN - 1130-0108 UR - https://www.unboundmedicine.com/medline/citation/9090984/[Idiopathic_portal_hypertension_multiple_focal_nodular_hepatic_hyperplasia_the_CREST_syndrome_and_protein_S_deficiency]_ L2 - http://www.diseaseinfosearch.org/result/6003 DB - PRIME DP - Unbound Medicine ER -