[14 cases of communicating syringomyelia associated with Chiari I malformation in children].
Neurochirurgie. 1992; 38(5):297-303.N

Abstract

The authors review their experience of 14 children with syringomyelia and associated Chiari I malformation observed during the last 21 years. Initial symptoms were motor weakness (57%), sensory signs (50%), scoliosis (50%) and bladder dysfunction (21.5%), while signs of admission were pyramidal signs (78.5%) with motor deficit (43%), spinal deformities (64.2%), syringomyelic syndrome (36%) and sensory deficit (21.5%). Four children were investigated with myelography, three with myelography and spinal CT Scan and the last seven cases with MRI. Ten children (71.4%) underwent a decompression of the Chiari malformation with or without drainage of the cyst and shunting of an associated hydrocephalus. Syringo-peritoneal shunts were used in 3 children and laminectomy with syringo-subarachnoid shunt in 1 case. The neurological symptoms improved in 57% of the cases, 2 patients deteriorated and 4 patients were lost to follow-up. The authors discuss the clinical symptomatology, the MRI study, the controversies concerning the treatment and concluded with their attitude concerning this pathology in children.

Authors+Show Affiliations

Lena G
Service de Neurochirurgie Pédiatrique, Hôpital des Enfants de La Timone, Marseille.
Boudawara Z
No affiliation info available
Genitori L
No affiliation info available
Cavalhero S
No affiliation info available
Choux M
No affiliation info available

MeSH

AdolescentArnold-Chiari MalformationCerebrospinal Fluid ShuntsChildChild, PreschoolFemaleHumansLaminectomyMagnetic Resonance ImagingMaleSyringomyelia

Pub Type(s)

English Abstract
Journal Article

Language

fre

PubMed ID

1299775