[Primitive neuroectodermal tumor (PNET) of the upper-urinary tract].
Prog Urol. 2009 Sep; 19(8):579-81.PU

Abstract

Primitive neuroectodermal tumors (PNETs) are rare and aggressive malignant small round cell sarcomas. Primitive urogenital location of PNETs is rare and occurs most frequently in the kidney. PNETs of the upper-urinary tract are exceptional (only one case reported in the literature). Its diagnosis is almost postoperative within pathological study of the operatory specimen, supported by immunohistochemistry and cytogenetics. Treatment is similar in all to that of Ewing's sarcoma and involves surgery, chemotherapy and radiotherapy. We report a new case of upper-urinary tract PNET and discuss the diagnostic and therapeutic problems posed by this particular tumor.

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Authors+Show Affiliations

Ammani A
Service d'urologie, hôpital militaire d'instruction Mohammed-V, Hay-Riad, 10101 Rabat, Maroc. ammani-1@hotmail.com
Ghadouane M
No affiliation info available
Hajji F
No affiliation info available
Janane A
No affiliation info available
Ameur A
No affiliation info available
Abbar M
No affiliation info available

MeSH

AgedAntineoplastic Combined Chemotherapy ProtocolsHumansMaleNeuroectodermal Tumors, PrimitiveUrologic Neoplasms

Pub Type(s)

Case Reports
English Abstract
Journal Article

Language

fre

PubMed ID

19699458