Congenital lymphangioma circumscriptum of vulva presenting as multiple giant mass lesions: a case report and literature review.
J Obstet Gynaecol Res. 2018 May; 44(5):978-982.JO

Abstract

A G2L2 33-year-old woman presented to our clinic with large verrucous warty masses in labia major, perinea and the end portion of her spine measuring about 15 × 7, 9 × 7 and 8 × 8 cm, which had been enlarged following puberty and pregnancy. Her right upper and left lower limbs had gross congenital lymphedema. The masses were removed by superficial partial vulvectomy with a qualified margin and repaired without skin graft. Pathology report showed lymphangioma circumscriptum. Several months of follow up revealed normal healing and no recurrence. In conclusion, congenital vulvar lymphangioma, which is a rare disorder, can be highly triggered by hormonal-stimulating situations like puberty and pregnancy. Thus, it is better to visit the affected cases in a timely manner in order to excise these lesions before massive enlargement. In our experience, a superficial partial vulvectomy without skin graft can be a sufficient procedure. Obviously, an appropriate approach during and after surgery would be very important for obtaining a desirable healing.

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Authors+Show Affiliations

Akhavan S
Department of Gynecology Oncology, Vali-Asr Hospital, Tehran University of Medical Sciences, Tehran, Iran.
Agah J
Department of Obstetrics and Gynecology Oncology, Sabzevar University of Medical Sciences, Sabzevar, Iran.
Nili F
Department of Pathology, Cancer Institute, Imam Khomeini Hospital Complex, Tehran, Iran.

MeSH

AdultFemaleHumansLymphangiomaVulvar Neoplasms

Pub Type(s)

Case Reports

Language

eng

PubMed ID

29484773