Anterior Myelomeningocele presenting as a posterior mediastinal mass has rarely been described. These anomalies, characterized by protrusion of meninges and spinal cord through open vertebral arches, present with devastating spinal or neurological problems. We present the case of a young female with a chronic history of right upper abdominal pain and low grade fever but no associated neurological or spinal defects. Relevant investigations showed a posterior mediastinal mass in right paraspinal region. Through a right postero-lateral thoracotomy, complete excision of the growth with preservation of major surrounding structures was carried out. Histopathology revealed Myelomeningocele. To our knowledge, this is the only case of Anterior Myelomeningocele at the thoracic level without neurospinal involvement.