Cleidocranial dysplasia (CCD) is a rare congenital disease characterised by generalised skeletal and orofacial defects. The dental rehabilitation of patients with CCD is a case-sensitive procedure requiring a multidisciplinary approach.
A 24-year-old woman presented with the skeletal and oral manifestations of CCD, including multiple poorly erupted and impacted teeth. The patient was very depressed and rejected orthodontic treatment; therefore, we formulated a treatment plan involving extraction of all impacted and poorly erupted teeth under general anaesthesia, followed by fabrication and delivery of transitional complete dentures for cosmetic, functional, and psychological benefits. Three months later, 14 screw basal implants were inserted in the maxillary and mandibular jaws and subjected to immediate loading with fixed prostheses 3 days later. At the 3-year follow-up visit, the patient expressed satisfaction with the aesthetic and functional aspects of the prostheses and presented with excellent oral health.
The timing of diagnosis, patient's age, willingness to undergo the planned treatment, and treatment duration are valuable considerations for establishing an appropriate treatment plan for the oral manifestations of CCD.
To our knowledge, this is the first report on basal implant-based full-mouth rehabilitation in a patient with CCD. Basal implant-supported prostheses may be useful for patients with CCD who present with a limited bony foundation after tooth removal. The treatment requires lesser time than orthodontic treatment, eliminates the need for bone grafting, spares the patient from ill-ﬁtting dentures, reduces the overall cost, and improves the quality of life.