- [Acute urine retention due to herlyn-Werner-Wunderlinch syndrome.] [Journal Article]
- AEArch Esp Urol 2019; 72(5):530-534
- Herlyn-Werner-Wunderlich syndrome (HWW) is a rare congenital anomaly difficult to diagnose due to an alteration in the common embryological development of the reproductive and urinary tract, with ren…
Herlyn-Werner-Wunderlich syndrome (HWW) is a rare congenital anomaly difficult to diagnose due to an alteration in the common embryological development of the reproductive and urinary tract, with renal agenesis, double collecting system, renal duplication and horseshoe kidney as urologic abnormalities. Due to its rarity and associated urological alterations, we believe that the urologist should be aware of this syndrome because of its implications. MATERIAL AND METHODS: We present the case of an 18-year-old patient with acute retention of urine associated with Herlyn-Werner-Wunderlinch syndrome. We describe this syndrome after a bibliographic search. RESULTS: In our case, the initial clinical course was exclusively urological, with the presentation of voiding bladder dysfunction with subsequent acute retention of urine. Surgical treatment resolved the patient's initial complication. CONCLUSIONS: In this case, as in others, nonspecific and variable symptoms may delay the diagnosis, which may lead to late complications such as endometriosis, adhesion syndrome, collections and infertility. Treatment suppresses pain, improves reproductive capacity and prevents late complications.
- Unicornuate uterus with a rudimentary non-communicating cavitary horn in association with VACTERL association: case report. [Journal Article]
- BWBMC Womens Health 2019 May 30; 19(1):71
- CONCLUSIONS: We report yet the second case of VACTERL association and unicornuate uterus with non-communicating functional rudimentary horn, in hope of expanding the knowledge of a rare occurrence. This case also highlights the importance of considering the diagnosis of Müllerian duct anomalies in patients with a history of other anomalies, and/or history of early-age secondary dysmenorrhea.
- Successful Surgical Treatment for Congenital Vaginal Agenesis Accompanied by Functional Uterus: A Report of Two Cases. [Case Reports]
- GMGynecol Minim Invasive Ther 2019 Apr-Jun; 8(2):76-79
- We present two cases of congenital vaginal agenesis with functional uterine corpus, manifesting with periodic lower abdominal pain and hematometra in adolescence. Both patients were successfully trea…
We present two cases of congenital vaginal agenesis with functional uterine corpus, manifesting with periodic lower abdominal pain and hematometra in adolescence. Both patients were successfully treated with the creation of neovagina and neocanal structures to discharge menstrual blood; this may also facilitate the preservation of fertility. Both cases were characterized by degrees of congenital vaginal agenesis, whether short or completely absent, with no communication between the uterine cavity and external genitalia, as confirmed by physical examination and imaging. We surgically reconstructed a neovagina with the modified McIndoe's procedure, using an artificial skin graft, and canalized to the caudal portion of the uterine cavity. Although redilatation of the neocanal was required, no patient suffered severe infection in postoperative course and both now exhibit regular menstruation. Although hysterectomy has classically been the preferred treatment for such cases, recent technical progression enables treatment of such diseases with conservative and minimally invasive surgery, in a safe manner.
- Case Report of the Successful Use of Mirena Levonorgestrel Intrauterine System in a Patient with Didelphys Uterus and Obstructed Hemivagina. [Case Reports]
- JPJ Pediatr Adolesc Gynecol 2019; 32(2):182-185
- CONCLUSIONS: We report the successful use of the Mirena IUS in a patient with a Müllerian anomaly, supporting the use of this device in carefully selected patients.
- Urinary presentations of a posttraumatic vaginal septum in a 14-year-old girl. [Journal Article]
- TJTurk J Urol 2018; 44(5):441-444
- Obstructing lesions of vagina, such as transverse vaginal septum, are rare anomalies. In this paper, we report a case of posttraumatic transverse vaginal septum. The patient was a 14-year-old girl wh…
Obstructing lesions of vagina, such as transverse vaginal septum, are rare anomalies. In this paper, we report a case of posttraumatic transverse vaginal septum. The patient was a 14-year-old girl who had a transverse vaginal septum because of repaired perineal trauma happened during earthquake that hit Bam city of Iran, when she was three years old. Post-traumatic vaginal septum had resulted in development of a massive hematometra. To our knowledge, this is the first report of urinary incontinence due to massive hematometra, which resulted from a posttraumatic vaginal septum. The rareness and diversity of clinical presentations of vaginal obstructing lesions can lead to misdiagnosis. The patient might refer to different medical and surgical specialists. So, knowing the symptoms is necessary for its early diagnosis. The probability of vaginal obstructing lesions in peripubertal girls with lower urinary tract symptoms should always be considered.
- Müllerian Aplasia with Severe Hematometra: A Case Report of Diagnosis and Management in a Low Resource Setting. [Case Reports]
- JPJ Pediatr Adolesc Gynecol 2019; 32(2):189-192
- CONCLUSIONS: Diagnosis of vaginal and cervical agenesis is complicated in low-resource settings and treatment must be modified when subspecialty care and consistent follow-up are not available.
- Congenital anal atresia with rectovestibular fistula, scoliosis, unilateral renal agenesis, and finger defect (VACTERL association) in a patient with partial bicornuate uterus and distal vaginal atresia: A case report. [Case Reports]
- MMedicine (Baltimore) 2018; 97(45):e12822
- CONCLUSIONS: Clinicians should have a high index of suspicion when evaluating patients with genital malformations associated with VACTERL. Early diagnosis of distal vaginal atresia with appropriate surgical intervention decreases long-term morbidity.
- Treatment of cervical agenesis with minimally invasive therapy: Case report. [Case Reports]
- GMGynecol Minim Invasive Ther 2017 Oct-Dec; 6(4):202-204
- Cervical agenesis is very rare congenital disorder case with cervical not formed. Because of cervical clogged so that menstruation can not be drained. We Report the case of a19 years old women still …
Cervical agenesis is very rare congenital disorder case with cervical not formed. Because of cervical clogged so that menstruation can not be drained. We Report the case of a19 years old women still single with endometrioma, hematometra, cervical agenesis and perform surgery combination laparoscopy and transvaginally with laparoscopic cystectomy, neocervix, and use catheter no 24f in the new cervix. And now she can currently be normal menstruation. Minimally invasive theraphy of congenital anomalies case is recommended to save reproductive function.
- Uterine flexion suture: modified B-Lynch uterine compression suture for the treatment of uterine atony during cesarean section. [Journal Article]
- IJInt J Womens Health 2018; 10:487-492
- CONCLUSIONS: Uterine flexion suture technique, which was modified from the B-Lynch suture, was inexpensive, quick, and effective in the treatment of atonic postpartum uterus in women undergoing cesarean section.
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- Pre-, intra-, and postoperative management of Robert's uterus. [Journal Article]
- FSFertil Steril 2018; 110(4):778-779
- CONCLUSIONS: Three-dimensional ultrasound techniques seem to be the best tool for complex pre- and postoperative management of Robert's uterus. Minimally invasive ultrasound-guided hysteroscopic metroplasty should be considered as the first choice of treatment because of the potential for normalization of uterine morphology and function.