A Rare Intradural Extramedullary Neurenteric Cyst in the Cervical Spine.Iran J Child Neurol 2026; 20(2):61-64.IJ
Neurenteric cysts (NCs), also known as endodermal cysts, are rare congenital lesions of endodermal origin. They were thought to originate from a failure of dissolution of the neurenteric canal between the notochord and endoderm during the third week of embryogenesis. The primary clinical symptoms differ from focal pain to paresthesia and weakness based on the cyst's location. This study presents a case of intradural extramedullary NC of the spine at the cervical level. A 10-year-old boy was referred to the hospital, with neck pain and weakness in his left hand. Imaging studies revealed fusion of cervical vertebrae at the levels of C3-C4 and C5-C6. On MRI, a cystic lesion in the intradural extramedullary region compressing the cord was evident. As the preferred treatment option, surgical total resection was completed through the posterior approach, and the definitive diagnosis was made based on the histochemical analysis. NC is a rare lesion and should be kept in mind as a differential diagnosis. Surgical intervention, particularly total resection, frequently improves the sensory and motor deficits associated with NC and is the treatment of choice.
