Sideroblastic Anemias
General Principles
Definition
Sideroblastic anemias are hereditary or acquired RBC disorders characterized by abnormal iron metabolism associated with the presence of ring sideroblasts (RS) in the developing RBCs in the BM.
Etiology
- Acquired
- Primary sideroblastic anemia (myelodysplastic syndrome with ring sideroblasts [MDS-RS] or myelodysplastic/myeloproliferative neoplasms with ring sideroblasts [MDS/MPN-RS]).
- Secondary sideroblastic anemia is caused by drugs (i.e., chloramphenicol, cycloserine, ethanol, isoniazid, pyrazinamide), lead or zinc toxicity, chronic alcohol use, or copper deficiency.
- Hereditary
- X-linked
- Autosomal
- Mitochondrial
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Citation
Bhat, Pavat, et al., editors. "Sideroblastic Anemias." Washington Manual of Medical Therapeutics, 35th ed., Wolters Kluwer Health, 2016. The Washington Manual, www.unboundmedicine.com/washingtonmanual/view/Washington-Manual-of-Medical-Therapeutics/602385/all/Sideroblastic_Anemias.
Sideroblastic Anemias. In: Bhat PP, Dretler AA, Gdowski MM, et al, eds. Washington Manual of Medical Therapeutics. Wolters Kluwer Health; 2016. https://www.unboundmedicine.com/washingtonmanual/view/Washington-Manual-of-Medical-Therapeutics/602385/all/Sideroblastic_Anemias. Accessed December 5, 2023.
Sideroblastic Anemias. (2016). In Bhat, P., Dretler, A., Gdowski, M., Ramgopal, R., & Williams, D. (Eds.), Washington Manual of Medical Therapeutics (35th ed.). Wolters Kluwer Health. https://www.unboundmedicine.com/washingtonmanual/view/Washington-Manual-of-Medical-Therapeutics/602385/all/Sideroblastic_Anemias
Sideroblastic Anemias [Internet]. In: Bhat PP, Dretler AA, Gdowski MM, Ramgopal RR, Williams DD, editors. Washington Manual of Medical Therapeutics. Wolters Kluwer Health; 2016. [cited 2023 December 05]. Available from: https://www.unboundmedicine.com/washingtonmanual/view/Washington-Manual-of-Medical-Therapeutics/602385/all/Sideroblastic_Anemias.
* Article titles in AMA citation format should be in sentence-case
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ED - Dretler,Alexandra,
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ED - Ramgopal,Rajeev,
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